parkinsonism due to ATP13A2 deficiency

ORPHA: 314632

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with parkinsonism due to ATP13A2 deficiency, sourced from HPO and Orphanet clinical annotations.

RigidityDystoniaMyoclonusTremorBradykinesiaPostural instabilityDiffuse cerebral atrophyParkinsonism with favorable response to dopaminergic medicationBabinski signUpgaze palsyCognitive impairmentDysarthriaGait disturbanceMuscle weaknessAbnormal caudate nucleus morphologyFatigueDepressionPostural tremor

Classification & Codes

Orphanet Code

ORPHA:314632
parkinsonism due to ATP13A2 deficiency
OrphanetORPHA:314632
Treatments0 drug(s)
Symptoms on record18 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO