paternal uniparental disomy of chromosome 6

ORPHA: 96191

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with paternal uniparental disomy of chromosome 6, sourced from HPO and Orphanet clinical annotations.

Joint hypermobilityCryptorchidismLabial hypertrophyMacroglossiaGingival overgrowthHigh palateSmall anterior fontanelleProminent occiputAbnormality of the faceRetrognathiaMicrognathiaAbnormal earlobe morphologyProminent noseShallow orbitsPrecocious pubertyNeonatal insulin-dependent diabetes mellitusIntrauterine growth retardationUmbilical herniaOligohydramniosVentricular septal defectCardiomegalyHypoplastic fingernailDehydrationGeneralized myoclonic seizureHepatomegalyNeonatal respiratory distressPostnatal growth retardationPatent ductus arteriosusAbdominal wall defectAbnormal placenta morphology

Classification & Codes

Orphanet Code

ORPHA:96191
paternal uniparental disomy of chromosome 6
OrphanetORPHA:96191
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO