pauci-immune glomerulonephritis
ORPHA: 93126
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with pauci-immune glomerulonephritis, sourced from HPO and Orphanet clinical annotations.
GlomerulonephritisRenal insufficiencyProteinuriaMicroscopic hematuriaElevated circulating creatinine concentrationSmall vessel vasculitisDecreased glomerular filtration rateCytoplasmic antineutrophil antibody positivityGlomerular sclerosisAbnormality of the skinFeverAbnormality of the respiratory systemCrescentic glomerulonephritisAbnormality of the eyePurpuraHoarse voiceAcute kidney injuryTubulointerstitial nephritisAbdominal painAbnormality of the upper respiratory tractDyspneaArthralgiaAntinuclear antibody positivityAbnormality of the pulmonary vasculatureArteritisMacroscopic hematuriaNephrotic range proteinuriaCoughPulmonary hemorrhageOral ulcerAbnormality of the cardiovascular systemPancreatitisAbnormality of the gastrointestinal tractMultiple mononeuropathyScleritis
Classification & Codes
Orphanet Code
ORPHA:93126pauci-immune glomerulonephritis
| Orphanet | ORPHA:93126 |
| Treatments | 0 drug(s) |
| Symptoms on record | 35 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO