PELVIS syndrome

ORPHA: 83628

Overview

PELVIS is an acronym defining the association of Perineal hemangioma, External genitalia malformations, Lipomyelomeningocele, Vesicorenal abnormalities, Imperforate anus, and Skin tag. Eleven cases have been reported.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with PELVIS syndrome, sourced from HPO and Orphanet clinical annotations.

CryptorchidismHypospadiasBifid scrotumMicropenisHypoplastic labia majoraAmbiguous genitaliaRenal duplicationVesicoureteral refluxRenal agenesisBifid uterusHemangiomaAnal atresiaSpina bifidaMyelomeningoceleBladder exstrophyEctopic anusSkin tags

Classification & Codes

Orphanet Code

ORPHA:83628
PELVIS syndrome
OrphanetORPHA:83628
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
PELVIS syndrome | OrphanDrug