Pemphigus erythematosus
ICD-10: L10.4ORPHA: 79480
Overview
human disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Pemphigus erythematosus, sourced from HPO and Orphanet clinical annotations.
AutoimmunityLocalized skin lesionMalar rashErythematous plaqueAcantholysisAntinuclear antibody positivityAbnormal blistering of the skinLinear IgG deposits along the epidermal basement membrane zoneOral ulcerHypopigmented skin patchesSystemic lupus erythematosusFocal dermal aplasia/hypoplasiaAnti-neuromuscular Junction acetylcholine receptor antibody positivitySkin erosion
Classification & Codes
ICD-10 Code
L10.4Orphanet Code
ORPHA:79480Pemphigus erythematosus
| ICD-10 | L10.4 |
| Orphanet | ORPHA:79480 |
| Treatments | 0 drug(s) |
| Symptoms on record | 14 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO