Perioral myoclonia with absences

ORPHA: 139426

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Perioral myoclonia with absences, sourced from HPO and Orphanet clinical annotations.

Bilateral tonic-clonic seizureEEG with spike-wave complexesLoss of speechReduced consciousnessFocal seizure with eyelid myocloniaChin myoclonusIntellectual disabilityGeneralized non-motor (absence) seizureGeneralized myoclonic seizureFalls

Classification & Codes

Orphanet Code

ORPHA:139426
Perioral myoclonia with absences
OrphanetORPHA:139426
Treatments0 drug(s)
Symptoms on record10 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO