Pfeiffer syndrome type 1

ORPHA: 93258

Overview

Pfeiffer syndrome type 1 (PS1) is a mild to moderately severe type of Pfeiffer syndrome (PS; see this term), characterized by bicoronal craniosynostosis, variable finger and toe malformations, and in most cases, normal intellectual development

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Pfeiffer syndrome type 1, sourced from HPO and Orphanet clinical annotations.

High palateBrachycephalyHypertelorismHigh foreheadHearing impairmentLow-set earsProptosisToe syndactylyShort footAqueductal stenosisShort noseShort palmDepressed nasal bridgeFinger syndactylyHallux varusAplasia/Hypoplasia of the thumbBroad hallux phalanxShort halluxBroad thumbBicoronal synostosisMidface retrusion

Classification & Codes

Orphanet Code

ORPHA:93258
Pfeiffer syndrome type 1
OrphanetORPHA:93258
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO