Pfeiffer syndrome type 3

ORPHA: 93260

Overview

Pfeiffer syndrome type 3 (PS3) is a severe type of Pfeiffer syndrome (PS; see this term), characterized by bicoronal craniosynostosis, severe associated functional disorders, and hand, foot and elbow abnormalities

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Pfeiffer syndrome type 3, sourced from HPO and Orphanet clinical annotations.

Vesicoureteral refluxHorseshoe kidneyHydronephrosisCleft palateHigh palateBrachyturricephalyHypertelorismHigh foreheadHearing impairmentLow-set earsStenosis of the external auditory canalChoanal atresiaProptosisAmblyopiaIntellectual disabilitySeizureLimitation of joint mobilityLaryngomalaciaToe syndactylyShort footAnal atresiaRespiratory distressChiari malformationAqueductal stenosisIncreased intracranial pressureIntestinal malrotationTracheomalaciaShort noseDepressed nasal bridgeFinger syndactylyHallux varusBroad hallux phalanxShort halluxBroad thumbMidface retrusionSmall hand

Classification & Codes

Orphanet Code

ORPHA:93260
Pfeiffer syndrome type 3
OrphanetORPHA:93260
Treatments0 drug(s)
Symptoms on record36 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO