pituitary deficiency due to empty sella turcica syndrome

ORPHA: 91354

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with pituitary deficiency due to empty sella turcica syndrome, sourced from HPO and Orphanet clinical annotations.

ImpotenceOligomenorrheaHeadacheDecreased response to growth hormone stimulation testPrecocious pubertyIncreased circulating prolactin concentrationSeizureAbnormal cerebrospinal fluid morphologyAutoimmunityReduced visual acuityPituitary hypothyroidismAbnormality of mental functionAdrenocorticotropic hormone deficiencyVisual acuity test abnormalityHypopituitarismDiplopiaCentral diabetes insipidusHypotensionHyponatremiaTrigeminal neuralgia

Classification & Codes

Orphanet Code

ORPHA:91354
pituitary deficiency due to empty sella turcica syndrome
OrphanetORPHA:91354
Treatments0 drug(s)
Symptoms on record20 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO