polycystic kidney disease 2

ORPHA: 730

Overview

autosomal dominant polycystic kidney disease that has material basis in autosomal dominant inheritance of mutation in the PKD2 gene on chromosome 4q22.1

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with polycystic kidney disease 2, sourced from HPO and Orphanet clinical annotations.

Renal insufficiencyRenal cystHepatic cystsElevated circulating creatinine concentrationDecreased glomerular filtration rateHematuriaHypertensionStage 5 chronic kidney diseaseAbnormal urinary electrolyte concentrationAlbuminuriaChronic kidney diseaseFlank painRecurrent urinary tract infectionsEnlarged kidneyUric acid nephrolithiasisMitral valve prolapsePancreatic cystsAortic root aneurysmDilatation of the cerebral arteryPolycystic liver diseaseCalcium oxalate nephrolithiasisAbnormal systemic arterial morphologyReduced sperm motilityPyelonephritisArachnoid cystPituitary growth hormone cell adenoma

Classification & Codes

Orphanet Code

ORPHA:730
polycystic kidney disease 2
OrphanetORPHA:730
Treatments0 drug(s)
Symptoms on record26 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO