posterior urethral valve
ICD-10: Q64.2ORPHA: 93110
Overview
congenital disorder of urinary system
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with posterior urethral valve, sourced from HPO and Orphanet clinical annotations.
Aplasia/Hypoplasia of the lungsFetal pyelectasisDilatation of the bladderFetal megacystisPyelonephritisUrinary retentionLethargyOligohydramniosUrethral stenosisDysuriaRecurrent urinary tract infectionsCongenital posterior urethral valveChronic kidney diseaseVesicoureteral refluxHydronephrosisBladder outlet obstructionBladder diverticulumUrinary incontinenceRenal insufficiencyProteinuriaRenal dysplasiaHematuriaHypertensionPotter faciesAbdominal painLow back painStage 5 chronic kidney disease
Classification & Codes
ICD-10 Code
Q64.2Orphanet Code
ORPHA:93110posterior urethral valve
| ICD-10 | Q64.2 |
| Orphanet | ORPHA:93110 |
| Treatments | 0 drug(s) |
| Symptoms on record | 27 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO