posttransplant acute limbic encephalitis

ORPHA: 163921

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with posttransplant acute limbic encephalitis, sourced from HPO and Orphanet clinical annotations.

SeizureMemory impairmentHyponatremiaIncreased CSF protein concentrationEEG with focal epileptiform dischargesCSF polymorphonuclear pleocytosisViremiaHyperglycorrhachiaSepsisCSF lymphocytic pleiocytosisAtypical behaviorPsychosisDepressionAnxietyAtaxiaConfusionDystoniaMyoclonusEEG with abnormally slow frequenciesAbnormal autonomic nervous system physiologyAbnormal hippocampus morphologyAbnormality of movementCognitive impairment

Classification & Codes

Orphanet Code

ORPHA:163921
posttransplant acute limbic encephalitis
OrphanetORPHA:163921
Treatments0 drug(s)
Symptoms on record23 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO