PPoma
ORPHA: 97278
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with PPoma, sourced from HPO and Orphanet clinical annotations.
Neoplasm of the pancreasNeoplasm of the small intestineAbnormal abdomen morphologyWeight lossDiarrheaNausea and vomitingConstipationAnorexiaHepatomegalyEpisodic abdominal painPoor appetiteHypoactive bowel soundsIntermittent jaundiceCholelithiasisIntrahepatic cholestasisAscitesGastrointestinal hemorrhageIntestinal obstructionIntestinal carcinoidExtrahepatic cholestasisLack of bowel soundsAbnormality of the thyroid glandIncreased circulating gonadotropin levelElevated circulating growth hormone concentrationIncreased circulating prolactin concentrationSubcutaneous lipomaPituitary adenomaParathyroid adenomaHypercalcemiaIncreased circulating cortisol levelPrimary hyperparathyroidismAdrenocortical adenoma
Classification & Codes
Orphanet Code
ORPHA:97278PPoma
| Orphanet | ORPHA:97278 |
| Treatments | 0 drug(s) |
| Symptoms on record | 32 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO