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primary angiitis of the central nervous system

MeSH: C535276ORPHA: 140989

Contents

  1. 1. Overview
  2. 2. Available Treatments
  3. 3. Clinical Presentation
  4. 4. Classification & Codes

Overview

autoimmune disease of the cerebral arteries

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with primary angiitis of the central nervous system, sourced from HPO and Orphanet clinical annotations.

Cerebral vasculitisHemiparesisStrokeNausea and vomitingHeadacheTransient ischemic attackAphasiaParalysisMultifocal cerebral white matter abnormalitiesRecurrent subcortical infarctsCSF pleocytosisAbnormal CSF protein concentrationCognitive impairmentBlurred visionDiplopiaSeizureAtaxiaDysarthriaFeverIntracranial hemorrhageTetraparesisParaparesisReduced visual acuityTransient global amnesiaAbnormal visual field testPseudopapilledemaParkinsonismVertigoConstitutional symptomAmaurosis fugax

Classification & Codes

MeSH Code

C535276

Orphanet Code

ORPHA:140989
primary angiitis of the central nervous system
MeSHC535276
OrphanetORPHA:140989
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO