Primary Biliary Cholangitis
ICD-10: DB95.0MeSH: D015209ORPHA: 186
Overview
A chronic autoimmune liver disease characterized by progressive destruction of intrahepatic bile ducts leading to cholestasis and cirrhosis. Predominantly affects middle-aged women and has a prevalence of approximately 1 in 3,000-4,000 individuals.
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Primary Biliary Cholangitis, sourced from HPO and Orphanet clinical annotations.
Hyperpigmentation of the skinCirrhosisBiliary cirrhosisConjugated hyperbilirubinemiaDermatographic urticariaAntimitochondrial antibody positivityAbnormality of the thyroid glandJaundicePruritusXanthelasmaOrthostatic hypotensionHepatic fibrosisHepatic failureHepatocellular carcinomaPortal hypertensionHepatomegalyRecurrent fungal infectionsAutoimmunityAbnormal circulating lipid concentrationHypercholesterolemiaElevated circulating alkaline phosphatase concentrationAntinuclear antibody positivityIncreased circulating IgM levelAbnormal intrahepatic bile duct morphologyOnychomycosisElevated gamma-glutamyltransferase levelOsteoporosisExcessive daytime somnolenceAscitesSplenomegalyEsophageal varixSleep disturbanceHepatic encephalopathySteatorrheaCeliac diseaseHypoalbuminemiaIncreased circulating IgA concentrationAbdominal distentionHepatitisFatigueGastrointestinal inflammation
Classification & Codes
ICD-10 Code
DB95.0MeSH Code
D015209Orphanet Code
ORPHA:186Primary Biliary Cholangitis
| ICD-10 | DB95.0 |
| MeSH | D015209 |
| Orphanet | ORPHA:186 |
| Treatments | 0 drug(s) |
| Symptoms on record | 41 signs |
| Status | published |
Factual Authority
Last Updated3/21/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO