primary ciliary dyskinesia 37

ORPHA: 244

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with primary ciliary dyskinesia 37, sourced from HPO and Orphanet clinical annotations.

Chronic otitis mediaRecurrent otitis mediaNasal congestionChronic rhinitisNeonatal respiratory distressMale infertilityRecurrent sinopulmonary infectionsChronic sinusitisRespiratory tract infectionAbnormal sperm motilityProductive coughAbnormal sputumNasal polyposisAbnormality of the genitourinary systemHearing impairmentConductive hearing impairmentDelayed speech and language developmentAbnormality of the skeletal systemClubbingAbnormal heart morphologySitus inversus totalisMorphological central nervous system abnormalityBronchiectasisAirway obstructionFemale infertilityRecurrent mycobacterial infectionsPulmonary situs ambiguusPeribronchovascular interstitial thickeningAbnormal cardiovascular system morphologyWheezingLithoptysisAtelectasisHydrocephalusRod-cone dystrophyTransposition of the great arteriesDouble outlet right ventricleAspleniaPolyspleniaVentriculomegalyIntestinal malrotationRespiratory failurePersistent left superior vena cavaAnomalous pulmonary venous returnAbnormal atrial arrangementAtrial situs ambiguousAbnormal inferior vena cava morphology

Classification & Codes

Orphanet Code

ORPHA:244
primary ciliary dyskinesia 37
OrphanetORPHA:244
Treatments0 drug(s)
Symptoms on record46 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
primary ciliary dyskinesia 37 | OrphanDrug