primary coenzyme Q10 deficiency 6

ORPHA: 280406

Overview

primary coenzyme Q10 deficiency that has material basis in an autosomal recessive mutation of COQ6 on chromosome 14q24.3

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

Orphanet Code

ORPHA:280406
primary coenzyme Q10 deficiency 6
OrphanetORPHA:280406
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO