primary effusion lymphoma

ICD-10: C83.8MeSH: D054685ORPHA: 48686

Contents

1. Overview
2. Available Treatments
3. Clinical Presentation
4. Classification & Codes

Overview

Primary effusion lymphoma (PEL) is a large B-cell lymphoma located in the body cavities, characterized by pleural, peritoneal, and pericardial fluid lymphomatous effusions and that is always associated with human herpes virus-8 (HHV-8)

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with primary effusion lymphoma, sourced from HPO and Orphanet clinical annotations.

Pericardial effusionAbdominal painDyspneaPleural effusionAbnormal peritoneum morphologyImmunodeficiencyAbdominal distentionB-cell lymphoma

Classification & Codes

ICD-10 Code

C83.8

MeSH Code

D054685

Orphanet Code

ORPHA:48686

primary effusion lymphoma

ICD-10	`C83.8`
MeSH	`D054685`
Orphanet	`ORPHA:48686`
Treatments	0 drug(s)
Symptoms on record	8 signs
Status	published

Factual Authority

Last Updated3/20/2026

Clinical DataHPO · Orphanet

Drug DataFDA · EMA · CDSCO