primary hyperoxaluria

MeSH: D006960ORPHA: 416

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with primary hyperoxaluria, sourced from HPO and Orphanet clinical annotations.

HyperoxaluriaCalcium oxalate nephrolithiasisNephrocalcinosisAbnormality of the dentitionRetinopathyOptic disc pallorOptic atrophyHematuriaFailure to thriveMetabolic acidosisBone painRecurrent fracturesElevated circulating hepatic transaminase concentrationIntermittent claudicationGeneralized osteosclerosisAbnormal dental pulp morphologyReduced visual acuityPeripheral neuropathyRootless teethChoroidal neovascularizationAciduriaChronic kidney diseaseHeart blockArterial occlusionRaynaud phenomenonElevated urine glycolateGangreneAcrocyanosisHypercalciuriaStage 5 chronic kidney diseaseCutis marmorataCardiomyopathyCalcinosis cutis

Classification & Codes

MeSH Code

D006960

Orphanet Code

ORPHA:416
primary hyperoxaluria
MeSHD006960
OrphanetORPHA:416
Treatments0 drug(s)
Symptoms on record33 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO