Primary membranoproliferative glomerulonephritis

ORPHA: 54370

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Primary membranoproliferative glomerulonephritis, sourced from HPO and Orphanet clinical annotations.

Membranoproliferative glomerulonephritisRenal insufficiencyProteinuriaNephrotic syndromeHypertensionMicroscopic hematuriaGlomerular subendothelial electron-dense depositsDecreased circulating complement C3 concentrationChronic kidney diseaseC3 nephritic factor positivityAcute kidney injuryHypoalbuminemiaStage 5 chronic kidney diseaseMyocardial infarctionAbnormal thrombosisDrusen

Classification & Codes

Orphanet Code

ORPHA:54370
Primary membranoproliferative glomerulonephritis
OrphanetORPHA:54370
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO