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primary pulmonary hypertension

MeSH: D065627ORPHA: 422

Contents

  1. 1. Overview
  2. 2. Available Treatments
  3. 3. Clinical Presentation
  4. 4. Classification & Codes

Overview

chronic pulmonary heart disease characterized by an increase of blood pressure in the pulmonary artery, pulmonary vein, or pulmonary capillaries, among others, has symptoms shortness of breath, dizziness, fainting, leg swelling

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with primary pulmonary hypertension, sourced from HPO and Orphanet clinical annotations.

Pulmonary arterial hypertensionDyspneaAbnormal cardiovascular system physiologySyncopePalpitationsHepatomegalyRight ventricular dilatationTricuspid regurgitationFatigueHeart murmurElevated jugular venous pressureChest painPedal edema

Classification & Codes

MeSH Code

D065627

Orphanet Code

ORPHA:422
primary pulmonary hypertension
MeSHD065627
OrphanetORPHA:422
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO