primary sclerosing cholangitis
MeSH: C536419ORPHA: 171
Overview
sclerosing cholangitis characterized by fibroobliterative inflammation of the biliary tract, leading to cirrhosis and portal hypertension
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with primary sclerosing cholangitis, sourced from HPO and Orphanet clinical annotations.
CholestasisAutoimmunityAbnormal biliary tract morphologyCirrhosisHepatic fibrosisPortal hypertensionHepatosplenomegalyAscitesSplenomegalyWeight lossFeverHepatomegalyElevated circulating hepatic transaminase concentrationElevated alkaline phosphatase of hepatic originSpider hemangiomaAbnormal large intestine physiologyDilated superficial abdominal veinsUlcerative colitisPalmar telangiectasiaRenal insufficiencyDepressionOsteopeniaOsteoporosisJaundicePruritusCholelithiasisHepatocellular carcinomaCongestive heart failurePancreatitisAbdominal painPleural effusionCeliac diseaseHypoalbuminemiaPolyclonal elevation of IgMGeneralized amyotrophyReduced circulating vitamin A concentrationProlonged prothrombin timeDecreased circulating vitamin K concentrationHepatitisFatigueCholangiocarcinomaAdenocarcinoma of the large intestineDecreased circulating vitamin D concentrationDecreased circulating vitamin E concentrationChronic hepatic failureThyroiditisType I diabetes mellitusUveitisEncephalopathyAcute hepatic failureNeoplasm of the gallbladder
Classification & Codes
MeSH Code
C536419Orphanet Code
ORPHA:171primary sclerosing cholangitis
| MeSH | C536419 |
| Orphanet | ORPHA:171 |
| Treatments | 0 drug(s) |
| Symptoms on record | 51 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO