progressive supranuclear palsy

MeSH: D013494ORPHA: 683

Overview

neurodegenerative disease characterized by supranuclear gaze palsy, postural instability, progressive rigidity, and mild dementia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with progressive supranuclear palsy, sourced from HPO and Orphanet clinical annotations.

Supranuclear gaze palsySupranuclear ophthalmoplegiaDysphagiaPostural instabilityUnsteady gaitFallsNeuronal loss in central nervous systemAbnormal synaptic transmissionImpulsivityVisual impairmentVertical supranuclear gaze palsySlow saccadic eye movementsBlepharospasmEmotional labilityDepressionIrritabilityApathyDelayed speech and language developmentDysarthriaDystoniaBradykinesiaCerebral cortical atrophyGliosisPseudobulbar signsVertigoMemory impairmentAphasiaCognitive impairmentAbnormality of eye movementDementiaTremorRigidity

Classification & Codes

MeSH Code

D013494

Orphanet Code

ORPHA:683
progressive supranuclear palsy
MeSHD013494
OrphanetORPHA:683
Treatments0 drug(s)
Symptoms on record32 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO