progressive supranuclear palsy-parkinsonism syndrome

MeSH: C537240ORPHA: 240085

Overview

PSP-parkinsonism (PSP-P) is an atypical variant of progressive supranuclear palsy (PSP; see this term), a rare late-onset neurodegenerative disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with progressive supranuclear palsy-parkinsonism syndrome, sourced from HPO and Orphanet clinical annotations.

BradykinesiaAxial muscle stiffnessRigidityTremorAbnormality of eye movementMental deteriorationFallsPostural instabilityRespiratory distressNeuromuscular dysphagiaDystoniaParkinsonism with favorable response to dopaminergic medicationApathyDepressionImpaired visuospatial constructive cognitionVertical supranuclear gaze palsyAbnormal saccadic eye movementsAbnormal speech patternMemory impairment

Classification & Codes

MeSH Code

C537240

Orphanet Code

ORPHA:240085
progressive supranuclear palsy-parkinsonism syndrome
MeSHC537240
OrphanetORPHA:240085
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO