pseudohypoaldosteronism type 2

ORPHA: 757

Overview

Pseudohypoaldosteronism type 2 (PHA2) is a rare inherited form of hypertension characterized by hyperkalemia, hyperchloremic metabolic acidosis, normal or elevated aldosterone, low renin, and normal renal function

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with pseudohypoaldosteronism type 2, sourced from HPO and Orphanet clinical annotations.

Abnormality of the dentitionAbnormal dental enamel morphologyHypertensionMuscle weaknessGrowth delayNausea and vomitingHyperkalemiaPeriodic paralysisShort stature

Classification & Codes

Orphanet Code

ORPHA:757
pseudohypoaldosteronism type 2
OrphanetORPHA:757
Treatments0 drug(s)
Symptoms on record9 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO