pseudoxanthomatous diffuse cutaneous mastocytosis

ORPHA: 280794

Overview

Pseudoxanthomatous diffuse cutaneous mastocytosis (PDCM) is a rare form of diffuse cutaneous mastocytosis (DCM; see this term) characterized by yellow-orange infiltrated and xanthogranuloma-like lesions with only limited blistering

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with pseudoxanthomatous diffuse cutaneous mastocytosis, sourced from HPO and Orphanet clinical annotations.

Abnormal blistering of the skinCutaneous mastocytosis

Classification & Codes

Orphanet Code

ORPHA:280794
pseudoxanthomatous diffuse cutaneous mastocytosis
OrphanetORPHA:280794
Treatments0 drug(s)
Symptoms on record2 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
pseudoxanthomatous diffuse cutaneous mastocytosis | OrphanDrug