pulmonary capillary hemangiomatosis

MeSH: C535861ORPHA: 199241

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with pulmonary capillary hemangiomatosis, sourced from HPO and Orphanet clinical annotations.

LymphadenopathyPulmonary capillary hemangiomatosisCapillary malformationGround-glass opacificationInterlobular septal thickeningDecreased DLCOCyanosisRight ventricular failureDyspneaHemoptysisExertional dyspneaElevated pulmonary artery pressurePedal edemaHemothoraxHypoxemiaCentrilobular ground-glass opacification on pulmonary HRCTDiffuse alveolar hemorrhageAbnormal pulmonary vein morphologyMediastinal lymphadenopathyClubbing of fingersPleural effusionPulmonary edemaPericardial effusion

Classification & Codes

MeSH Code

C535861

Orphanet Code

ORPHA:199241
pulmonary capillary hemangiomatosis
MeSHC535861
OrphanetORPHA:199241
Treatments0 drug(s)
Symptoms on record23 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO