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pulmonary hypertension, primary, 1

ORPHA: 422

Contents

  1. 1. Overview
  2. 2. Available Treatments
  3. 3. Clinical Presentation
  4. 4. Classification & Codes

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with pulmonary hypertension, primary, 1, sourced from HPO and Orphanet clinical annotations.

Pulmonary arterial hypertensionDyspneaAbnormal cardiovascular system physiologySyncopePalpitationsHepatomegalyRight ventricular dilatationTricuspid regurgitationFatigueHeart murmurElevated jugular venous pressureChest painPedal edema

Classification & Codes

Orphanet Code

ORPHA:422
pulmonary hypertension, primary, 1
OrphanetORPHA:422
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO