refractory celiac disease

ORPHA: 398063

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with refractory celiac disease, sourced from HPO and Orphanet clinical annotations.

Villous atrophyChronic diarrheaWeight lossMalabsorptionMicrocytic anemiaOsteoporosisElevated circulating hepatic transaminase concentrationAbnormality of the nervous systemInflammatory abnormality of the skinAutoimmune antibody positivityIncreased proportion of HLA DR+ CD4+ T cellsHypocalcemiaHypoproteinemiaHypomagnesemiaHypophosphatemiaIron deficiency anemiaNormocytic anemiaMacrocytic anemiaElevated alkaline phosphatase of bone originLow serum calcitriolAbnormal spleen physiologyAbdominal painMalnutritionArthralgiaJejunitisProtein-losing enteropathyHypoalbuminemiaLymphoma

Classification & Codes

Orphanet Code

ORPHA:398063
refractory celiac disease
OrphanetORPHA:398063
Treatments0 drug(s)
Symptoms on record28 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO