Respiratory bronchiolitis interstitial lung disease
ORPHA: 79127
Overview
medical condition
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Respiratory bronchiolitis interstitial lung disease, sourced from HPO and Orphanet clinical annotations.
Restrictive ventilatory defectDyspneaEmphysemaDiffuse reticular or finely nodular infiltrationsChronic pulmonary obstructionGround-glass opacificationWheezingReduced FEV1/FVC ratioInspiratory cracklesChronic bronchitisHypersensitivity pneumonitisRespiratory tract infectionHypoxemiaNonproductive coughDecreased DLCOClubbingWeight lossFeverHemoptysisBronchiectasisHoneycomb lungChest pain
Classification & Codes
Orphanet Code
ORPHA:79127Respiratory bronchiolitis interstitial lung disease
| Orphanet | ORPHA:79127 |
| Treatments | 0 drug(s) |
| Symptoms on record | 22 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO