retinitis pigmentosa

MeSH: D012174ORPHA: 791

Overview

retinal degeneration characterized by the gradual deterioration of the photoreceptors or the retinal pigment epithelium of the retina leading to progressive sight loss

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with retinitis pigmentosa, sourced from HPO and Orphanet clinical annotations.

Conductive hearing impairmentSensorineural hearing impairmentVisual impairmentAbnormal electroretinogramRetinal degenerationPhotophobiaBlindnessNystagmusOptic atrophyProgressive night blindnessAbnormal retinal pigmentationSpicular pigmentation of the retinaAbnormal retinal vascular morphologyGlaucomaOptic disc pallorKeratoconusOphthalmoplegiaNyctalopiaHyperinsulinemiaRetinal atrophyPosterior subcapsular cataractAttenuation of retinal blood vesselsPeripheral visual field lossCystoid macular edemaOptic disc drusenAbnormal full-field electroretinogramAbnormal central response of multifocal electroretinogramPhotoreceptor outer segment loss on macular OCTColor vision defectReduced visual acuityPhotopsia

Classification & Codes

MeSH Code

D012174

Orphanet Code

ORPHA:791
retinitis pigmentosa
MeSHD012174
OrphanetORPHA:791
Treatments0 drug(s)
Symptoms on record31 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO