retroperitoneal fibrosis
ICD-10: K66.2MeSH: D012185ORPHA: 49041
Overview
progressive condition characterized by deposition of fibrous tissue in the retroperitoneal space
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with retroperitoneal fibrosis, sourced from HPO and Orphanet clinical annotations.
Abdominal painAnorexiaIncreased blood urea nitrogenElevated circulating creatinine concentrationLow back painElevated erythrocyte sedimentation rateLarge vessel vasculitisElevated circulating C-reactive protein concentrationFatigueUnilateral renal hypoplasiaAnti-thyroid peroxidase antibody positivityFlank painDeep dermal perivascular inflammatory infiltrateUreteropelvic junction obstructionHashimoto thyroiditisRheumatoid arthritisPainRenal insufficiencyHydronephrosisHypertensionWeight lossNormocytic anemiaAcute kidney injuryFeverNausea and vomitingConstipationSystemic lupus erythematosusRheumatoid factor positiveAnti-smooth muscle antibody positivityAntineutrophil antibody positivityPsoriasiform dermatitisPedal edemaMembranous nephropathyHydrocele testisNephrotic syndromeHematuriaImpotenceBudd-Chiari syndromeRenal tubular epithelial necrosisVaricoceleRetrograde ejaculationDysuriaRenovascular hypertension
Classification & Codes
ICD-10 Code
K66.2MeSH Code
D012185Orphanet Code
ORPHA:49041retroperitoneal fibrosis
| ICD-10 | K66.2 |
| MeSH | D012185 |
| Orphanet | ORPHA:49041 |
| Treatments | 0 drug(s) |
| Symptoms on record | 43 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO