Reynolds syndrome

ORPHA: 779

Overview

Reynolds syndrome (RS) is an autoimmune disorder characterized by the association of primary biliary cirrhosis (PBC) with limited cutaneous systemic sclerosis (lcSSc) (see these terms)

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Reynolds syndrome, sourced from HPO and Orphanet clinical annotations.

XerostomiaJaundiceSkin rashPruritusKeratoconjunctivitis siccaArthritisCirrhosisAscitesFeverDysphagiaGastroesophageal refluxRespiratory insufficiencyHepatomegalyInfectious encephalitisMyalgiaAbnormal gastric mucosa morphologyIrregular hyperpigmentationGeneralized abnormality of skinSclerodactylyFatigueMucosal telangiectasiaeTelangiectasia of the skinLichenificationSkin ulcer

Classification & Codes

Orphanet Code

ORPHA:779
Reynolds syndrome
OrphanetORPHA:779
Treatments0 drug(s)
Symptoms on record24 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Reynolds syndrome | OrphanDrug