Robinow syndrome

MeSH: C562492ORPHA: 97360

Overview

syndrome characterized by mild to moderate short stature due to growth delays after birth, distinctive craniofacial abnormalities, skeletal malformations and genital abnormalities

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Robinow syndrome, sourced from HPO and Orphanet clinical annotations.

MesomeliaShort statureHypertelorismSmall for gestational ageAcromesomeliaExternal genital hypoplasiaMesomelic arm shorteningCryptorchidismSmall scrotumMicropenisHypoplastic labia majoraClitoral hypoplasiaHydronephrosisBroad alveolar ridgesOrofacial cleftTriangular mouthGingival overgrowthMacrocephalyLong philtrumMicrognathiaPosteriorly rotated earsLow-set earsFlared nostrilsBroad nasal tipAnteverted naresProptosisHypodontiaDental crowdingDental malocclusionTooth malpositionRib fusionMissing ribsBrachydactylySyndactylyAbnormal heart morphologyVentricular septal defectAtrial septal defectPulmonic stenosisCoarctation of aortaSmall nailFrontal bossingNail dysplasiaScoliosisKyphoscoliosisHemivertebraeShort noseDepressed nasal bridgeRadioulnar dislocationBifid distal phalanx of the thumbShort distal phalanx of fingerHigh anterior hairlineAnkyloglossiaBifid tonguePulmonary valve atresiaTricuspid atresiaMidface retrusionFused thoracic vertebraeWebbed penisMulticystic kidney dysplasiaMixed hearing impairmentUmbilical herniaMarked delay in eruption of permanent teethPersistence of primary teethNeurodevelopmental delayDecreased serum testosterone concentration

Classification & Codes

MeSH Code

C562492

Orphanet Code

ORPHA:97360
Robinow syndrome
MeSHC562492
OrphanetORPHA:97360
Treatments0 drug(s)
Symptoms on record65 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO