Rothmund-Thomson syndrome

MeSH: D011038ORPHA: 2909

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Rothmund-Thomson syndrome, sourced from HPO and Orphanet clinical annotations.

Skin rashPoikilodermaMalar rashAbnormality of the dentitionSparse eyelashesInfertilityAbnormality of the skeletal systemSmall for gestational ageShort statureReduced bone mineral densityPlantar hyperkeratosisReticular hyperpigmentationAbnormal blistering of the skinSparse hairPalmar hyperkeratosisSparse eyebrowFacial edemaCarious teethAbnormal dental enamel morphologyDelayed eruption of teethHypoplasia of teethMicrodontiaOsteopeniaHypopigmentation of the skinJuvenile cataractSelective tooth agenesisAbnormal nail morphologySmall nailAbnormality of blood and blood-forming tissuesVomitingDiarrheaNail dysplasiaIncreased susceptibility to fracturesHypoplasia of the ulnaBroad ulnaAplasia/Hypoplasia of the patellaAplasia/Hypoplasia of the radiusAplasia/Hypoplasia of the skinNeoplasm of the skinShort thumbSupernumerary toothMetaphyseal striationsTelangiectasia of the skinAbnormal trabecular bone morphologyDecreased total neutrophil countAnemiaLeukemiaAplastic anemiaBasal cell carcinomaSquamous cell carcinomaMelanomaMyelodysplasiaCalcinosisAlopecia totalisNasogastric tube feeding in infancyPorokeratosis

Classification & Codes

MeSH Code

D011038

Orphanet Code

ORPHA:2909
Rothmund-Thomson syndrome
MeSHD011038
OrphanetORPHA:2909
Treatments0 drug(s)
Symptoms on record56 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO