Schöpf–Schulz–Passarge syndrome

ICD-10: Q82.8MeSH: C565607ORPHA: 221039

Overview

SchC6pf-Schulz-Passarge syndrome (SSPS) is a rare autosomal recessive ectodermal dysplasia characterized by multiple eyelid apocrine hidrocystomas, palmoplantar keratoderma, hypotrichosis, hypodontia and nail dystrophy

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

Q82.8

MeSH Code

C565607

Orphanet Code

ORPHA:221039
Schöpf–Schulz–Passarge syndrome
ICD-10Q82.8
MeSHC565607
OrphanetORPHA:221039
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Schöpf–Schulz–Passarge syndrome | OrphanDrug