Seckel syndrome

ORPHA: 808

Overview

autosomal recessive disease characterized by intrauterine growth retardation and postnatal dwarfism with microcephaly and intellectual disability

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Seckel syndrome, sourced from HPO and Orphanet clinical annotations.

MicrocephalyNarrow faceMicrognathiaConvex nasal ridgeIntellectual disabilityCraniosynostosisIntrauterine growth retardationSandal gapDelayed skeletal maturationClinodactyly of the 5th fingerShort statureCachexiaPrematurely aged appearanceMild global developmental delayCognitive impairmentAbnormal earlobe morphologyAbsent earlobeDownslanted palpebral fissuresGlaucomaAbnormal dental enamel morphologyHip dysplasiaSparse scalp hairTooth agenesisCone-shaped epiphysisScoliosisJoint hypermobility

Classification & Codes

Orphanet Code

ORPHA:808
Seckel syndrome
OrphanetORPHA:808
Treatments0 drug(s)
Symptoms on record26 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO