secondary intestinal lymphangiectasia
ORPHA: 90363
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with secondary intestinal lymphangiectasia, sourced from HPO and Orphanet clinical annotations.
LymphedemaIncreased stool alpha1-antitrypsin concentrationEdemaDecreased total lymphocyte countMalabsorptionChronic diarrheaHypocholesterolemiaIntestinal lymphedemaSecondary hyperaldosteronismFatigueCirrhosisFeverVomitingPleural effusionConstrictive pericarditisCeliac diseaseLymphomaDecreased circulating IgA concentrationDecreased circulating total IgMAutoimmunityHypoalbuminemiaDecreased circulating immunoglobulin concentrationAbdominal colicHypofibrinogenemiaAnasarcaChylous ascitesFood intoleranceDecreased circulating prealbumin concentrationGastrointestinal eosinophiliaDecreased circulating IgG1 concentrationReduced circulating transferrin concentrationSclerodermaRight ventricular failureThromboembolismIntussusceptionVolvulusIntestinal bleedingRecurrent infectionsIntestinal obstructionB-cell lymphoma
Classification & Codes
Orphanet Code
ORPHA:90363secondary intestinal lymphangiectasia
| Orphanet | ORPHA:90363 |
| Treatments | 0 drug(s) |
| Symptoms on record | 40 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO