semantic dementia

ORPHA: 100069

Overview

progressive neurodegenerative disorder

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with semantic dementia, sourced from HPO and Orphanet clinical annotations.

AphasiaBrain atrophyVisual agnosiaAnomic aphasiaDementiaAbnormal speech patternDyslexiaAlexiaDysgraphiaAbulia

Classification & Codes

Orphanet Code

ORPHA:100069
semantic dementia
OrphanetORPHA:100069
Treatments0 drug(s)
Symptoms on record10 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO