Shapiro syndrome

MeSH: C537594ORPHA: 29822

Overview

Spontaneous periodic hypothermia (SPH) is a neurological disorder characterized by spontaneous periodic hypothermia and hyperhidrosis in the absence of hypothalamic lesions

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Shapiro syndrome, sourced from HPO and Orphanet clinical annotations.

HyperhidrosisPallorSkin rashSeizureAtaxiaGait disturbanceTremorDiarrheaNausea and vomitingHypothermiaSleep disturbanceAbnormal pattern of respirationReduced consciousnessAplasia/Hypoplasia of the corpus callosumArrhythmiaFatigue

Classification & Codes

MeSH Code

C537594

Orphanet Code

ORPHA:29822
Shapiro syndrome
MeSHC537594
OrphanetORPHA:29822
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO