short QT syndrome

ICD-10: R94.3MeSH: C580439ORPHA: 51083

Overview

heart conduction disease that is characterized by heart arrhythmia defined as a short QT interval on an EKG (less than 300 ms) that does not significantly change with heart rate, tall and peaked T waves, and a structurally normal heart

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with short QT syndrome, sourced from HPO and Orphanet clinical annotations.

Shortened QT intervalBradycardiaPalpitationsAtrial fibrillationSyncopeSudden cardiac deathVentricular fibrillationAtrioventricular blockVentricular arrhythmiaFatigueDyspneaHeart arrhythmiaPalpitation

Classification & Codes

ICD-10 Code

R94.3

MeSH Code

C580439

Orphanet Code

ORPHA:51083
short QT syndrome
ICD-10R94.3
MeSHC580439
OrphanetORPHA:51083
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO