short-rib thoracic dysplasia 9 with or without polydactyly

MeSH: C535463ORPHA: 140969

Overview

asphyxiating thoracic dystrophy that has material basis in homozygous or compound heterozygous mutation in the IFT140 gene on chromosome 16p13

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

MeSH Code

C535463

Orphanet Code

ORPHA:140969
short-rib thoracic dysplasia 9 with or without polydactyly
MeSHC535463
OrphanetORPHA:140969
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO