Silver-Russell syndrome

MeSH: D056730ORPHA: 813

Overview

growth disorder

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Silver-Russell syndrome, sourced from HPO and Orphanet clinical annotations.

Triangular faceLow-set earsBlue scleraeIntrauterine growth retardationShort statureCachexiaRelative macrocephalyPostnatal growth retardationProminent foreheadFeeding difficultiesCryptorchidismAbnormal male external genitalia morphologyThin vermilion borderDelayed cranial suture closureMicrognathiaDental crowdingInsulin resistanceMotor delayFailure to thrive in infancyAbnormally high-pitched voicePremature birthRecurrent hypoglycemiaConstipationGastroesophageal refluxSleep disturbanceDownturned corners of mouthDelayed skeletal maturationArthralgiaDecreased muscle massClinodactyly of the 5th fingerAbnormality of the calcaneusDecreased testicular sizeShoulder dimpleAbnormal appendicular skeleton morphologyPremature adrenarcheAsymmetric growthLower limb asymmetryUpper limb asymmetryHypospadiasAbnormality of the urinary systemAbnormal vagina morphologyAutistic behaviorPrecocious pubertyCafe-au-lait spotHyperhidrosisMild intellectual disabilityObesityAbnormality of the cardiovascular systemSandal gapScoliosisSecondary microcephalyGeneralized neonatal hypotoniaPosteriorly rotated ears

Classification & Codes

MeSH Code

D056730

Orphanet Code

ORPHA:813
Silver-Russell syndrome
MeSHD056730
OrphanetORPHA:813
Treatments0 drug(s)
Symptoms on record53 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO