Silver-Russell syndrome due to a point mutation

ORPHA: 397590

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Silver-Russell syndrome due to a point mutation, sourced from HPO and Orphanet clinical annotations.

Triangular faceMicrognathiaIntrauterine growth retardationSmall for gestational ageClinodactyly of the 5th fingerRelative macrocephalyFeeding difficulties in infancyPostnatal growth retardationProminent foreheadAbnormal scrotum morphologyHypospadiasCleft palateLow-set earsDelayed speech and language developmentSyndactylyMotor delayOligohydramniosAbnormality of the cardiovascular systemShort 5th fingerInguinal herniaCryptorchidismBifid scrotumHypothyroidismCafe-au-lait spotGlobal developmental delayHypoplastic fingernailHypoglycemiaFrontal bossingAsthmaSmall placentaAttention deficit hyperactivity disorderPolydactylyMicrophallusEctrodactylyAsymmetric growthDysmenorrhea

Classification & Codes

Orphanet Code

ORPHA:397590
Silver-Russell syndrome due to a point mutation
OrphanetORPHA:397590
Treatments0 drug(s)
Symptoms on record36 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO