Sinus venosus atrial septal defect

ICD-10: Q21.1MeSH: C548009ORPHA: 99105

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Sinus venosus atrial septal defect, sourced from HPO and Orphanet clinical annotations.

Left-to-right shuntPalpitationsExertional dyspneaExercise intoleranceAnomalous pulmonary venous returnFatigueCardiac conduction abnormalityParadoxical splitting of the second heart soundSystolic heart murmurAtrial arrhythmiaPulmonary arterial hypertensionDyspneaAtrial flutterSupraventricular tachycardiaAtrial fibrillationSupraventricular arrhythmiaRight ventricular dilatationTricuspid regurgitationPremature atrial contractionsAutomatic atrial tachycardiaFirst degree atrioventricular blockComplete right bundle branch blockJunctional ectopic tachycardiaStrokeCongestive heart failureThromboembolismAirway obstruction

Classification & Codes

ICD-10 Code

Q21.1

MeSH Code

C548009

Orphanet Code

ORPHA:99105
Sinus venosus atrial septal defect
ICD-10Q21.1
MeSHC548009
OrphanetORPHA:99105
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO