Sinus venosus atrial septal defect
ICD-10: Q21.1MeSH: C548009ORPHA: 99105
Overview
human disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Sinus venosus atrial septal defect, sourced from HPO and Orphanet clinical annotations.
Left-to-right shuntPalpitationsExertional dyspneaExercise intoleranceAnomalous pulmonary venous returnFatigueCardiac conduction abnormalityParadoxical splitting of the second heart soundSystolic heart murmurAtrial arrhythmiaPulmonary arterial hypertensionDyspneaAtrial flutterSupraventricular tachycardiaAtrial fibrillationSupraventricular arrhythmiaRight ventricular dilatationTricuspid regurgitationPremature atrial contractionsAutomatic atrial tachycardiaFirst degree atrioventricular blockComplete right bundle branch blockJunctional ectopic tachycardiaStrokeCongestive heart failureThromboembolismAirway obstruction
Classification & Codes
ICD-10 Code
Q21.1MeSH Code
C548009Orphanet Code
ORPHA:99105Sinus venosus atrial septal defect
| ICD-10 | Q21.1 |
| MeSH | C548009 |
| Orphanet | ORPHA:99105 |
| Treatments | 0 drug(s) |
| Symptoms on record | 27 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO