spastic tetraplegia-thin corpus callosum-progressive postnatal microcephaly syndrome

ORPHA: 447997

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spastic tetraplegia-thin corpus callosum-progressive postnatal microcephaly syndrome, sourced from HPO and Orphanet clinical annotations.

Delayed speech and language developmentIntellectual disabilityHyperreflexiaHypotoniaMotor delayHypertoniaDysphagiaLower limb spasticityHypoplasia of the corpus callosumSecondary microcephalyPrimary microcephalyBrain atrophyUrinary incontinenceHypertelorismLow-set earsProtruding earWide nasal bridgeSynophrysMotor stereotypyIrritabilityHyperactivityAbnormal facial shapeGastroesophageal refluxBilateral tonic-clonic seizureClonusRecurrent respiratory infectionsHypsarrhythmiaMultiple joint contracturesMyoclonic spasmsDepressed nasal bridgeCerebral hypomyelinationGastrostomy tube feeding in infancyHair-pullingInfantile spasms

Classification & Codes

Orphanet Code

ORPHA:447997
spastic tetraplegia-thin corpus callosum-progressive postnatal microcephaly syndrome
OrphanetORPHA:447997
Treatments0 drug(s)
Symptoms on record34 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO