spinocerebellar ataxia

ICD-10: G11.1MeSH: D020754ORPHA: 98757

Overview

group of dominantly inherited, predominately late-onset, cerebellar ataxias. Neuro-developmental outcome and brain-derived neurotrophic factor level in relation to feeding practice in early infancy.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spinocerebellar ataxia, sourced from HPO and Orphanet clinical annotations.

ProptosisProgressive external ophthalmoplegiaNystagmusDiplopiaDelayed speech and language developmentDysarthriaDystoniaHyperreflexiaAbnormality of extrapyramidal motor functionProgressive cerebellar ataxiaClumsinessSkeletal muscle atrophyAbnormal pyramidal signVocal cord paralysisAbnormal vestibular functionAbnormality of temperature regulation

Classification & Codes

ICD-10 Code

G11.1

MeSH Code

D020754

Orphanet Code

ORPHA:98757
spinocerebellar ataxia
ICD-10G11.1
MeSHD020754
OrphanetORPHA:98757
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
spinocerebellar ataxia | OrphanDrug