spinocerebellar ataxia type 11
ORPHA: 98767
Overview
Spinocerebellar ataxia type 11 (SCA11) is a subtype of autosomal dominant cerebellar ataxia type III (ADCA type III; see this term) characterized by the early-onset of cerebellar signs, eye movement abnormalities and pyramidal signs
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with spinocerebellar ataxia type 11, sourced from HPO and Orphanet clinical annotations.
Gait disturbanceHorizontal nystagmusDysarthriaDysphagiaProgressive cerebellar ataxiaGait imbalanceJerky ocular pursuit movementsVertical nystagmusDystoniaAbnormal pyramidal signPeripheral neuropathy
Classification & Codes
Orphanet Code
ORPHA:98767spinocerebellar ataxia type 11
| Orphanet | ORPHA:98767 |
| Treatments | 0 drug(s) |
| Symptoms on record | 11 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO