spinocerebellar ataxia type 17

MeSH: C564616ORPHA: 98759

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spinocerebellar ataxia type 17, sourced from HPO and Orphanet clinical annotations.

AtaxiaGait disturbanceTorticollisBlepharospasmAtypical behaviorSpasticityMental deteriorationCerebellar atrophyParkinsonismDystoniaRigidityChoreaNeuronal loss in central nervous systemInvoluntary movementsGeneralized cerebral atrophy/hypoplasiaAbnormal pyramidal signAtrophy/Degeneration affecting the brainstemCerebellar Purkinje layer atrophyWriter's cramp

Classification & Codes

MeSH Code

C564616

Orphanet Code

ORPHA:98759
spinocerebellar ataxia type 17
MeSHC564616
OrphanetORPHA:98759
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO