spinocerebellar ataxia type 20

MeSH: C537199ORPHA: 101110

Overview

Spinocerebellar ataxia type 20 (SCA20) is a very rare subtype of type I autosomal dominant cerebellar ataxia (ADCA type I; see this term). It is characterized by cerebellar dysarthria as the initial typical manifestation.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with spinocerebellar ataxia type 20, sourced from HPO and Orphanet clinical annotations.

DysarthriaCerebellar atrophyDysphoniaBradykinesiaCerebral calcificationHypermetric saccadesLaryngeal dystoniaTremor by anatomical siteGaze-evoked nystagmusAtaxiaHyperreflexiaGait ataxiaVertigoAbnormal pyramidal signUpper limb postural tremorDownbeat nystagmusIsometric tremorKinetic tremorIntention tremor

Classification & Codes

MeSH Code

C537199

Orphanet Code

ORPHA:101110
spinocerebellar ataxia type 20
MeSHC537199
OrphanetORPHA:101110
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO